Journalartikel
Autorenliste: Neuhaeuser, Christoph Armin; Kreymborg, Karsten Grosse; Mueller, Carsten; Khalil, Markus; Jux, Christian; Galambos, Csaba; Schranz, Dietmar
Jahr der Veröffentlichung: 2021
Seiten: 228-231
Zeitschrift: Journal of Pediatric Intensive Care
Bandnummer: 10
Heftnummer: 03
ISSN: 2146-4618
eISSN: 2146-4626
Open Access Status: Green
DOI Link: https://doi.org/10.1055/s-0040-1713437
Verlag: Thieme Publishing
Abstract:
A newborn infant patient presented with persistent pulmonary hypertension. For right ventricular decompression, the ductus arteriosus was kept open by prostaglandin E-1 infusion and was stented at the age of 4 weeks during heart catheterization. The child was weaned from mechanical ventilation, since pulmonary functions were adequate. A small atrial septal defect was identified and closed in cardiac catheterization laboratory to decrease preductal hypoxemia. Diagnostic workup led to the diagnosis of alveolar capillary dysplasia with misalignment of the pulmonary veins. Suprasystemic pulmonary arterial hypertension with persisting nitric oxide dependency remained the leading symptoms. The child underwent bilateral lung transplantation at the age of 28 months. He is well at the age of 44 months.
Zitierstile
Harvard-Zitierstil: Neuhaeuser, C., Kreymborg, K., Mueller, C., Khalil, M., Jux, C., Galambos, C., et al. (2021) Successful Management of an Infant with Atypical Presentation of Alveolar Capillary Dysplasia with Misalignment of the Pulmonary Veins, Journal of Pediatric Intensive Care, 10(03), pp. 228-231. https://doi.org/10.1055/s-0040-1713437
APA-Zitierstil: Neuhaeuser, C., Kreymborg, K., Mueller, C., Khalil, M., Jux, C., Galambos, C., & Schranz, D. (2021). Successful Management of an Infant with Atypical Presentation of Alveolar Capillary Dysplasia with Misalignment of the Pulmonary Veins. Journal of Pediatric Intensive Care. 10(03), 228-231. https://doi.org/10.1055/s-0040-1713437
Schlagwörter
alveolar capillary dysplasia; ductal stent; inhaled nitric oxide; POTTS SHUNT; pulmonary arterial hypertension; RIOCIGUAT