Journalartikel

Successful Management of an Infant with Atypical Presentation of Alveolar Capillary Dysplasia with Misalignment of the Pulmonary Veins


AutorenlisteNeuhaeuser, Christoph Armin; Kreymborg, Karsten Grosse; Mueller, Carsten; Khalil, Markus; Jux, Christian; Galambos, Csaba; Schranz, Dietmar

Jahr der Veröffentlichung2021

Seiten228-231

ZeitschriftJournal of Pediatric Intensive Care

Bandnummer10

Heftnummer03

ISSN2146-4618

eISSN2146-4626

Open Access StatusGreen

DOI Linkhttps://doi.org/10.1055/s-0040-1713437

VerlagThieme Publishing


Abstract
A newborn infant patient presented with persistent pulmonary hypertension. For right ventricular decompression, the ductus arteriosus was kept open by prostaglandin E-1 infusion and was stented at the age of 4 weeks during heart catheterization. The child was weaned from mechanical ventilation, since pulmonary functions were adequate. A small atrial septal defect was identified and closed in cardiac catheterization laboratory to decrease preductal hypoxemia. Diagnostic workup led to the diagnosis of alveolar capillary dysplasia with misalignment of the pulmonary veins. Suprasystemic pulmonary arterial hypertension with persisting nitric oxide dependency remained the leading symptoms. The child underwent bilateral lung transplantation at the age of 28 months. He is well at the age of 44 months.



Zitierstile

Harvard-ZitierstilNeuhaeuser, C., Kreymborg, K., Mueller, C., Khalil, M., Jux, C., Galambos, C., et al. (2021) Successful Management of an Infant with Atypical Presentation of Alveolar Capillary Dysplasia with Misalignment of the Pulmonary Veins, Journal of Pediatric Intensive Care, 10(03), pp. 228-231. https://doi.org/10.1055/s-0040-1713437

APA-ZitierstilNeuhaeuser, C., Kreymborg, K., Mueller, C., Khalil, M., Jux, C., Galambos, C., & Schranz, D. (2021). Successful Management of an Infant with Atypical Presentation of Alveolar Capillary Dysplasia with Misalignment of the Pulmonary Veins. Journal of Pediatric Intensive Care. 10(03), 228-231. https://doi.org/10.1055/s-0040-1713437



Schlagwörter


alveolar capillary dysplasiaductal stentinhaled nitric oxidePOTTS SHUNTpulmonary arterial hypertensionRIOCIGUAT


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