Journal article

A comparison between nailfold capillaroscopy patterns in adulthood in juvenile and adult-onset systemic sclerosis: A EUSTAR exploratory study


Authors listIngegnoli, Francesca; Boracchi, Patrizia; Gualtierotti, Roberta; Smith, Vanessa; Cutolo, Maurizio; Foeldvari, Ivan; Airo, Paolo; Jose Alegre-Sancho, Juan; Allanore, Yannick; Ananieva, Lidia P.; Ancuta, Codrina; Andrade, Luis Eduardo; Aringer, Martin; Becvar, Radim; Bojinca, Mihai; Butrimiene, Irena; Cantatore, Francesco Paolo; Caporali, Roberto; Caramaschi, Paola; Carreira, Patricia E.; Chirieac, Rodica; Corrado, Ada; Cosentino, Vanesa; Cuomo, Giovanna; Czirjak, Laszlo; Pereira Da Silva, Jose Antonio; de la Pena Lefebvre, Paloma Garcia; De Keyser, Filip; Mueller, Carolina de Souza; Damgaard, Kirsten; Damjanov, Nemanja; Denisov, Lev N.; Distler, Oliver; Doube, Alan; Dumitrascu, Alina; Engelhart, Merete; Exposito, Marta Valero; Eyerich, Kilian; Farge-Bancel, Dominique; Azevedo, Valderilio Feijo; Foti, Rosario; Frerix, Marc; Gabrielli, Armando; Garen, Torhild; Gottschalk, Paola; Groseanu, Laura; Guiducci, Serena; Guenther, Claudia; Hachulla, Eric; Hein, Ruediger; Heitmann, Stefan; Henes, Joerg; Hesselstrand, Roger; Highton, John; Lannone, Florenzo; Ionescu, Ruxandra Maria; Kayser, Cristiane; Karpec, Diana; Kerzberg, Eduardo; Kotulska, Anna; Kopec-Medrek, Magdalena; Kucharz, Eugene; Krummel-Lorenz, Brigitte; Lauffer, Felix; Launay, David; Li, Mengtao; Litinsky, Ira; Loyo, Esthela; Cerinic, Marco Matucci; Meroni, Pierluigi; Midtvedt, Oyvind; Mihai, Carmen Marina; Montecucco, Carlomaurizio; Montoya, Fabiana; Morgiel, Ewa; Mouthon, Luc; Mueller-Ladner, Ulf; Nielsen, Henrik; Opris, Daniela; Ortiz-Santamaria, Vera; Otsa, Kati; Pileckyte, Margarita; Pisarri, Simonetta; Popescu, Monica; Pozzi, Maria Rosa; Puppo, Francesco; Radominski, Sebastiao Cezar; Riccieri, Valeria; Rosato, Edoardo; Rozman, Blaz; Rubio, Silvia Rodriguez; Rugiene, Rita; Saar, Petra; Salvador, Maria Joao; Seidel, Matthias; Sokolik, Renata; Solanki, Kamal; Stamenkovic, Bojana; Stankovic, Aleksandra; Stebbings, Simon; Strauss, Gitte; Sulli, Alberto; Szamosi, Szilvia; Szechinski, Jacek; Szmyrka-Kaczmarek, Magdalena; Szuecs, Gabriella; Tanaseanu, Cristina-Mihaela; Tiglea, Isabela; Tyndall, Alan; Ughi, Nicola; Uprus, Maria; Vacca, Alessandra; Varju, Cecilia; Venalis, Algirdas; Venalis, Paulius; Walker, Ulrich A.; Widuchowska, Malgorzata; Wiland, Piotr; Wuttge, Dirk M.; Zeni, Silvana; Zenone, Thierry

Publication year2015

Pages19-24

JournalMicrovascular Research

Volume number102

ISSN0026-2862

eISSN1095-9319

DOI Linkhttps://doi.org/10.1016/j.mvr.2015.07.007

PublisherElsevier


Abstract

Objective: Qualitative capillaroscopy patterns in juvenile- and adult-onset systemic sclerosis (SSc) were studied in adulthood using data from the EULAR Scleroderma Trials and Research (EUSTAR) database.

Methods: Data collected between June 2004 and April 2013 were examined with focus on capillaroscopy. In this retrospective exploratory study, series of patients with juvenile-onset SSc were matched with series of adult-onset SSc having the same gender and autoantibody profile.

Results: 30 of 123 patients with juvenile-onset and 2108 of 7133 with adult-onset SSc had data on capillaroscopy. Juvenile-onset SSc showed scleroderma pattern more frequently than adult-onset SSc (93.3% and 88%). The OR was 2.44 and 95% Cl 0.57-10.41. An active scleroderma pattern was present in 58% of juvenile- and 61% of adult-onset SSc. The OR was 0.91 and 95% Cl 0.28-2.93. The late scleroderma pattern was present in 61% of juvenile- and 55.5% of adult-onset SSc. The OR was 1.06 and 95% Cl 0.34-3.56.

Conclusion: This is the first exploratory study on the comparison of capillaroscopy between juvenile- and adult-onset SSc in adulthood. Juvenile-onset SSc had an increase prevalence of sderoderma pattern, but a similar distribution of the three patterns was suggested. Further studies are needed to define this issue. (C) 2015 Elsevier Inc. All rights reserved.




Citation Styles

Harvard Citation styleIngegnoli, F., Boracchi, P., Gualtierotti, R., Smith, V., Cutolo, M., Foeldvari, I., et al. (2015) A comparison between nailfold capillaroscopy patterns in adulthood in juvenile and adult-onset systemic sclerosis: A EUSTAR exploratory study, Microvascular Research, 102, pp. 19-24. https://doi.org/10.1016/j.mvr.2015.07.007

APA Citation styleIngegnoli, F., Boracchi, P., Gualtierotti, R., Smith, V., Cutolo, M., Foeldvari, I., Airo, P., Jose Alegre-Sancho, J., Allanore, Y., Ananieva, L., Ancuta, C., Andrade, L., Aringer, M., Becvar, R., Bojinca, M., Butrimiene, I., Cantatore, F., Caporali, R., Caramaschi, P., ...Zenone, T. (2015). A comparison between nailfold capillaroscopy patterns in adulthood in juvenile and adult-onset systemic sclerosis: A EUSTAR exploratory study. Microvascular Research. 102, 19-24. https://doi.org/10.1016/j.mvr.2015.07.007



Keywords


CapillaroscopyCHILDHOOD RHEUMATIC-DISEASESEULAR SCLERODERMA TRIALSEUSTARJuvenile systemic sclerosisMicrocirculationNAILFOLD CAPILLAROSCOPYORGAN INVOLVEMENTSystemic sclerosisUPDATEVIDEOCAPILLAROSCOPY

Last updated on 2025-02-04 at 01:57